Systemic Vasculopathies: Imaging and Management

Systemic vasculopathies represent a wide spectrum of heterogeneous vascular disorders characterized by variable target vessel involvement, vascular abnormalities, and end organ damage. The revised 2012 Chapel Hill Consensus Conference scheme classifies systemic vasculitis syndromes into primary systemic, secondary systemic, single-vessel, and variable-vessel vasculitis categories with associated management implications. Multimodality imaging not only allows diagnosis, characterization, and localization of vascular abnormalities but also permits evaluation of natural history and complications, thus, facilitating optimal patient management. This article discusses epidemiologic and radiologic characteristics of several common systemic vasculopathies with an emphasis on the role of endovascular therapy for management of select disorders.