Abstract
Congenital long-QT syndrome with 2:1 atrioventricular block presenting in the perinatal period is rare, has a poor prognosis, and leads to high risk for lethal ventricular arrhythmic events. An implantable cardioverter-defibrillator seems to be the most effective treatment in the prevention of arrhythmic sudden cardiac death in patients with long-QT syndrome. Technical limitations and risks associated with implantable cardioverter-defibrillators in asymptomatic infants is considered too great to justify use for primary prophylaxis against sudden cardiac death. In this case report we describe the first successful parental use of an automated external defibrillator prescribed for primary prophylaxis against sudden cardiac death in an infant with long-QT syndrome.
Original language | English (US) |
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Pages (from-to) | e526-e529 |
Journal | Pediatrics |
Volume | 118 |
Issue number | 2 |
DOIs | |
State | Published - Aug 2006 |
Externally published | Yes |
Keywords
- Automated external defibrillator
- Long-QT syndrome
- Sudden cardiac death
ASJC Scopus subject areas
- Pediatrics, Perinatology, and Child Health