Abstract
Triple A syndrome, formerly known as Allgrove syndrome (AS), is characterized by achalasia, alacrima and adrenal insufficiency. Here we report an adolescent male with adrenal insufficiency who developed severe malnutrition secondary to a delayed diagnosis of achalasia. The severe malnutrition in our patient led to superior mesenteric artery (SMA) obstruction syndrome. Severe malnutrition to the point of SMA syndrome has not been previously described in the literature in Triple A syndrome.
Original language | English (US) |
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Pages (from-to) | 1221-1224 |
Number of pages | 4 |
Journal | Journal of Pediatric Endocrinology and Metabolism |
Volume | 29 |
Issue number | 10 |
DOIs | |
State | Published - Oct 1 2016 |
Keywords
- Triple A syndrome
- adrenal insufficiency
- malnutrition
ASJC Scopus subject areas
- Pediatrics, Perinatology, and Child Health
- Endocrinology, Diabetes and Metabolism
- Endocrinology