Functional hemispherotomy in Rasmussen syndrome in the absence of classic MRI findings

Yasunori Nagahama, Charuta Joshi, Brian Dlouhy, Angela Y. Wu, Taylor J. Abel, Gary Baumbach, Hiroto Kawasaki

Research output: Contribution to journalArticlepeer-review

2 Scopus citations


A 7-year-old previously healthy girl presented with a left-sided focal seizure without impaired consciousness and subsequently developed epilepsia partialis continua. Initial MRI was normal, and the subsequent images only showed a focal T2/FLAIR hyperintense area without cortical atrophy. She was diagnosed with Rasmussen syndrome by pathology and promptly treated with functional hemispherotomy. Rasmussen syndrome is a rare progressive neurological disorder, the only definitive cure for which is hemispheric disconnection. The disease presents a management dilemma, especially early in disease course without characteristic neuroimaging features. A high index of suspicion, multidisciplinary approach, and clear timely communication with the family are critical.

Original languageEnglish (US)
Pages (from-to)24-27
Number of pages4
JournalEpilepsy and Behavior Case Reports
StatePublished - 2017
Externally publishedYes


  • Early diagnosis
  • Functional hemispherectomy
  • Peri-insular functional hemispherotomy
  • Rasmussen syndrome
  • Rasmussen's encephalitis

ASJC Scopus subject areas

  • Neurology
  • Clinical Neurology
  • Behavioral Neuroscience


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