Cyanosis and Stroke due to Functional Cor Triatriatum Dexter in a Neonate

Rachel L. León, Nicholas B. Zaban, Marcus S. Schamberger, Chang Y. Ho, Ulrike Mietzsch

Research output: Contribution to journalArticlepeer-review

1 Scopus citations


Small remnants of the right valve of the sinus venosus are commonly found in adults, but the incidence and risk associated with these embryonic remnants in neonates are not well studied. The following report describes a cyanotic neonate with a large Eustachian valve remnant creating a functional cor triatriatum dexter who was initially diagnosed with persistent pulmonary hypertension of the newborn. The cyanosis in this infant improved over the first postnatal week with conservative management, but she suffered multifocal subcortical stroke, likely related to her intracardiac shunt. The clinical presentation and questions regarding long-term management of this rare diagnosis are explored.

Original languageEnglish (US)
Pages (from-to)231-234
Number of pages4
Issue number3
StatePublished - Mar 1 2018
Externally publishedYes


  • Congenital heart disease
  • Cor triatriatum dexter
  • Embryonic remnant
  • Neonatal hypoxia
  • Right valve of the sinus venosus

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Developmental Biology


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