Tricuspid atresia with absent pulmonary valve and intact ventricular septum: A rare association

Thomas H. Best; Himesh V. Vyas; Robert D B Jaquiss; Ritu Sachdeva

doi:10.1111/j.1747-0803.2010.00477.x

Tricuspid atresia with absent pulmonary valve and intact ventricular septum: A rare association

Thomas H. Best, Himesh V. Vyas, Robert D B Jaquiss, Ritu Sachdeva

Research output: Contribution to journal › Article › peer-review

9 Scopus citations

Abstract

The absence of the pulmonary valve in connection with tricuspid atresia and intact ventricular septum is a rare malformation, associated with a poor prognosis. The right ventricle is severely hypertrophied, resembling a cardiac mass protruding into the left ventricular outflow tract. We report such a case that underwent successful palliation with a Blalock-Taussig shunt followed by a superior cavopulmonary anastomosis.

Original language	English (US)
Pages (from-to)	393-396
Number of pages	4
Journal	Congenital Heart Disease
Volume	6
Issue number	4
DOIs	https://doi.org/10.1111/j.1747-0803.2010.00477.x
State	Published - Jul 1 2011

Keywords

Absent pulmonary valve
Cardiac tumor
Left ventricular outflow obstruction
Right ventricular dysplasia
Three dimensional echocardiography
Tricuspid atresia

ASJC Scopus subject areas

Pediatrics, Perinatology, and Child Health
Surgery
Radiology Nuclear Medicine and imaging
Cardiology and Cardiovascular Medicine

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10.1111/j.1747-0803.2010.00477.x

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abstract = "The absence of the pulmonary valve in connection with tricuspid atresia and intact ventricular septum is a rare malformation, associated with a poor prognosis. The right ventricle is severely hypertrophied, resembling a cardiac mass protruding into the left ventricular outflow tract. We report such a case that underwent successful palliation with a Blalock-Taussig shunt followed by a superior cavopulmonary anastomosis.",

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AU - Sachdeva, Ritu

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AB - The absence of the pulmonary valve in connection with tricuspid atresia and intact ventricular septum is a rare malformation, associated with a poor prognosis. The right ventricle is severely hypertrophied, resembling a cardiac mass protruding into the left ventricular outflow tract. We report such a case that underwent successful palliation with a Blalock-Taussig shunt followed by a superior cavopulmonary anastomosis.

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KW - Cardiac tumor

KW - Left ventricular outflow obstruction

KW - Right ventricular dysplasia

KW - Three dimensional echocardiography

KW - Tricuspid atresia

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Tricuspid atresia with absent pulmonary valve and intact ventricular septum: A rare association

Abstract

Keywords

ASJC Scopus subject areas

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