Pulmonary atresia with ventricular septal defect

Asad A. Shah, John F. Rhodes, Robert D.B. Jaquiss

Research output: Chapter in Book/Report/Conference proceedingChapter

2 Scopus citations


The management of patients with pulmonary atresia with ventricular septal defect is complex, in correspondence with the array of anatomic subtypes, and within subtypes there is substantial controversy about the optimal management strategy. In this chapter an overview of the most commonly encountered subtypes of PA-VSD will be presented, along with a review of the pathophysiology and presentation of the these subtypes, a description of the options for management, and a brief review of the outcomes for the variety of treatments which have been proposed.

Original languageEnglish (US)
Title of host publicationPediatric and Congenital Cardiology, Cardiac Surgery and Intensive Care
PublisherSpringer-Verlag London Ltd
Number of pages16
ISBN (Electronic)9781447146193
ISBN (Print)9781447146186
StatePublished - Jan 1 2014


  • Central shunt
  • Coil occlusion of aortopulmonary collaterals
  • Congenital heart disease
  • Cutting balloon angioplasty
  • DiGeorge syndrome
  • Major aortopulmonary collateral arteries
  • Nakata index
  • Neonatal heart surgery
  • Percutaneous pulmonary valve replacement
  • Pulmonary artery stenosis
  • Pulmonary artery stent
  • Pulmonary atresia
  • Right ventricle-to-pulmonary artery conduit
  • Systemic shunt
  • Tetralogy of Fallot
  • Unifocalization
  • Velo-cardio-facial syndrome
  • Ventricular septal defect

ASJC Scopus subject areas

  • Medicine(all)


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