Abstract
Sudden death is often the first manifestation in inherited cardiac arrhythmia syndromes. Patients with long QT syndrome who have an episode of syncope while on beta-blockade should be offered an implantable cardioverter-defibrillator (ICD). In Brugada syndrome and hypertrophic cardiomyopathy, ICDs are often the most effective treatment of primary and secondary prevention of cardiac arrest. Risk stratification is crucial in identifying those at greatest risk to provide lifesaving therapy with an ICD while avoiding complications in those unlikely to receive benefit.
Original language | English (US) |
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Pages (from-to) | 305-318 |
Number of pages | 14 |
Journal | Cardiology clinics |
Volume | 32 |
Issue number | 2 |
DOIs | |
State | Published - May 2014 |
Keywords
- Arrhythmogenic right ventricular cardiomyopathy
- Brugada syndrome
- Channelopathy
- Genetic syndrome
- Hypertrophic cardiomyopathy
- Long QT syndrome
- Sudden death
ASJC Scopus subject areas
- Cardiology and Cardiovascular Medicine