Abstract
Opinion statement: Fontan type palliations are a group of operations employed in patients with only one functional ventricle. These procedures take the normally parallel pulmonary and systemic circulations and place them in series to reestablish separation between the two. The Fontan circulation established by such operations is a unique, artificial physiologic entity. Although the Fontan circulation supports patients for decades, patients eventually experience progressive heart failure. As this growing group of patients reaches adulthood, there is a need for general cardiologists as well as adult congenital heart disease specialists to be familiar with the long-term sequelae of the Fontan circulation. The purpose of the present review is to summarize the limited available data on heart failure of the Fontan, its natural history, evaluation, and management.
Original language | English (US) |
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Pages (from-to) | 587-601 |
Number of pages | 15 |
Journal | Current Treatment Options in Cardiovascular Medicine |
Volume | 15 |
Issue number | 5 |
DOIs | |
State | Published - Oct 2013 |
Externally published | Yes |
Keywords
- Congenital heart disease
- Congestive heart failure
- Fontan
- Single ventricle
- Univentricle
ASJC Scopus subject areas
- Cardiology and Cardiovascular Medicine