TY - JOUR
T1 - Congenital atrophic dermatofibrosarcoma protuberans in a 7-month-old boy treated with Mohs micrographic surgery
AU - Feramisco, Jamison
AU - Larsen, Fiona
AU - Weitzul, Sarah
AU - Cockerell, Clay
AU - Ghali, Fred
PY - 2008/7/1
Y1 - 2008/7/1
N2 - Dermatofibrosarcoma protuberans is a rare, malignant, slow-growing, locally invasive tumor of the skin. Although most cases are acquired and diagnosed in adulthood, there have been an increasing number of congenital dermatofibrosarcoma protuberans mimicking benign birthmarks described in the literature. The clinical presentation of this tumor is often one of an indurated exophytic plaque or nodule; however, a rare variant can present as atrophic or sclerotic in nature. We report a case of congenital atrophic dermatofibrosarcoma protuberans of the groin in a 7-month-old boy, successfully treated with Mohs micrographic surgery.
AB - Dermatofibrosarcoma protuberans is a rare, malignant, slow-growing, locally invasive tumor of the skin. Although most cases are acquired and diagnosed in adulthood, there have been an increasing number of congenital dermatofibrosarcoma protuberans mimicking benign birthmarks described in the literature. The clinical presentation of this tumor is often one of an indurated exophytic plaque or nodule; however, a rare variant can present as atrophic or sclerotic in nature. We report a case of congenital atrophic dermatofibrosarcoma protuberans of the groin in a 7-month-old boy, successfully treated with Mohs micrographic surgery.
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U2 - 10.1111/j.1525-1470.2008.00718.x
DO - 10.1111/j.1525-1470.2008.00718.x
M3 - Article
C2 - 18789087
AN - SCOPUS:49349113786
SN - 0736-8046
VL - 25
SP - 455
EP - 459
JO - Pediatric Dermatology
JF - Pediatric Dermatology
IS - 4
ER -