TY - JOUR
T1 - Atypical Presentation of Extranodal Rosai-Dorfman Disease
AU - Prendes, Brandon L.
AU - Brinkman, William T.
AU - Sengupta, Anita L.
AU - Bavaria, Joseph E.
PY - 2009/2
Y1 - 2009/2
N2 - We describe a 42-year-old woman with progressive dyspnea on exertion resulting from pulmonary artery compression by a mediastinal mass due to extranodal Rosai-Dorfman disease. After initial biopsies were inconclusive, she underwent surgical resection of the mass to relieve the pulmonary artery compression, which was causing severe right ventricular dysfunction. Debulking of the mass required resection and reconstruction of the ascending aorta, pulmonary trunk, and bilateral pulmonary arteries using cardiopulmonary bypass and circulatory arrest. We believe this is the first report of Rosai-Dorfman disease manifesting as compression of the thoracic great vessels.
AB - We describe a 42-year-old woman with progressive dyspnea on exertion resulting from pulmonary artery compression by a mediastinal mass due to extranodal Rosai-Dorfman disease. After initial biopsies were inconclusive, she underwent surgical resection of the mass to relieve the pulmonary artery compression, which was causing severe right ventricular dysfunction. Debulking of the mass required resection and reconstruction of the ascending aorta, pulmonary trunk, and bilateral pulmonary arteries using cardiopulmonary bypass and circulatory arrest. We believe this is the first report of Rosai-Dorfman disease manifesting as compression of the thoracic great vessels.
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U2 - 10.1016/j.athoracsur.2008.07.037
DO - 10.1016/j.athoracsur.2008.07.037
M3 - Article
C2 - 19161795
AN - SCOPUS:58249136822
SN - 0003-4975
VL - 87
SP - 616
EP - 618
JO - Annals of Thoracic Surgery
JF - Annals of Thoracic Surgery
IS - 2
ER -